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 %2  Traitement des LAM de l adulte jeune (d"55 ans) en Tunisie Dr Ramzi Jeddi Service d hmatologie clinique HAO 7 sep 2007 4z&   >^E          Introduction $  Current treatment results for AML in younger adults(d"55-60 years) Study N CR(%) ED(%) OS(3-5yr) CALGB 474 72 9 34 GAMLCG 535 74 11 39 HOVON 253 77 7 38 ALFA 345 82 9 38&P4"   Historique $   Priode d tude 1997-2001 Patients (n) 202 Age (ans) 16-55(64%d"40) Cytogntique (%) RF 17 RI 66 RE 17 Traitement Htrogne (4 centres) e"2 conso (%) 57 Allo (n) 21 Auto (n) 5 LP""w " t   Historique $   Taux de RC 68% Absence de RC 32% .Rsistance 11% .Dcs 21% Rechute 55% SG (3,5ans) 26%, h 6 6!SG de toute la population$  7"#SG selon le nombre de consolidation$$$#  Conclusion de cette valuation$   1- Amliorer le taux de RC ( 68 %) 2- Diminuer dcs induction (21%) 3- Diminuer taux de rechute ( 55%) 4- Augmenter nombre d allogreffes 5- Prciser la place de l auto CSP 6- Mettre en place un protocole commun de prise en charge des LAM de l adulte en Tunisie &    Protocole national$  Induction IDA 12 mg/m2 j1-j3 + AraC 200 mg/m2 j1-j7 5 tudes randomises IDA vs DNR IDA>DNR (4 tudes) Berman E et al .Blood 1991 Wiernick PH et al.Blood 1992, Vogler WR et al JCO 1992 Reiffers j et al Leukemia 1996 J,/`        ?    M  C      G .Traitement post RC$   l ge, la cytogntique et l obtention ou non de la RC 3 groupes risque sont dfinis: - Groupe1: RC1 et cytogntique favorable -Groupe2: RC 1 induction et cytogntique intermdiaire -Groupe 3: non RC 1 induction et /ou cytogntique dfavorable v: -9bb d ?(Traitement post RC$"   8#LAP(M3)$  2 protocoles successifs (HAO) APL93 1997-2004 LPA99 Depuis 2004    Rsultats $      Patients (n) 30 Age(ans) 39(7-64) RC(%) 90 Dcs(%) 10 Rechute(%) 0 0Z  2LAM entre Jan 2003 et Dec 2006    185 LAM (18-55 ans) LAP LAM e >55 ans NE 87 30 22 29 17 Z$ M f]   vRsultats de ce protocole au service d hmatologie de l HAO<< ; 2 Priode d tude Jan03-Dec06 Patients(n) 87 Age(ans) 42(19-57) Cytogntique(%) RF 14 RI 76 RE 10 Traitement post induction(n) CT seule 49 CT +Auto(5) 54 Allo 13P V C   Rsultats $   2003-2006 1997-2001 RC(%) 1 cure 72 2 cures 77 68 Rsistance(%) 7 11 Dcs (%) (I) 16 22 (en RC) 14( 13 CT,23 Allo) ? infection 64 Rechutes (%) 39 55 ff$fff\= {  Survie sans rechute$   9&Survie sans rechute$ / Groupe sans donneur vs avec donneurD0  f / :$ Survie globale$ ;%Survie globale$   Cytogntique Age Immunophnotypage Pas d impact HVb  D 5 Rsultats MRC AML10$    4 Conclusion $  @)    La mdecine a fait depuis un sicle des progrs sans rpit, inventant par milliers des maladies nouvelles.  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A+S D ' = @B Dq ' = @BA?%,( < +O%,( < +DP' =%(%(D' =%(D' =A@BB2BB0B%()?D' =1:Bvisible*o3>+B#style.visibility<* <%(D' =+4 8?bCB#ppt_w+.3BCB#ppt_wB*Y3>B ppt_w<* <D' =+4 8?\CB#ppt_hBCB#ppt_hB*Y3>B ppt_h<* <D' =-g6B fade*<3<* <DP' =%(D' =%(D' =A@BB2BB0B%())?)D' =1:Bvisible*o3>+B#style.visibility<* <9%(D' =+4 8?bCB#ppt_w+.3BCB#ppt_wB*Y3>B ppt_w<* <9D' =+4 8?\CB#ppt_hBCB#ppt_hB*Y3>B ppt_h<* <9D' =-g6B fade*<3<* <9+p+0+ < ++0+ < +b 0 r(    0 P    `*     08     b*   d  c $ ?  >  0   0  vCliquez pour modifier les styles du texte du masque Deuxime niveau Troisime niveau Quatrime niveau Cinquime niveau4w   6 _P   `*     6l _   b*   H  0޽h ? 3380___PPT10.lV 0((    0Pn P   n `*     0n    n b*     6дn _P  n `*     6\n _  n b*   H  0޽h ? 3380___PPT10.lV  K0  0(  x  c $Tϯ <p  x  c $ϯ <    H  0޽h ? 33___PPT10i../ +D=' = @B +   K0 @ (  @r @ S $ 8 `}   r @ S  8  LB @ c $D ` LB @ c $D `` LB @ c $Dp``pH @ 0޽h ? 3fff___PPT10i./#+D=' = @B +=   K0 <4D(  Dr D S xO 8 `}   r D S ) 8` `P  LB D c $DPLB D c $DpPpH D 0޽h ? 3fff___PPT10i.0%k+D=' = @B +=   K0 <4 H(  Hr H S n 8 `}   r H S o 8 `  LB H c $DLB H c $DH H 0޽h ? 3fff___PPT10i.1鮎+D=' = @B +   K0 <G(  <r < S pz 8 `    < TA ? 8"Z ` ?0  < <|}P @  Q26%  < < P  f Mdiane=11 m     H < 0޽h ? 3fff___PPT10i.pL2(+D=' = @B +e   K0 d\@(  @r @ S  8    @ ZA ? 8c"$ `  @ <P `  d<2 conso  "   @ <\`  fe"2 conso  " @ <p0 Vp=0.0004   H @ 0޽h ? 3fff___PPT10i.+D=' = @B +   K0 `<(  ~  s * 8 `}   ~  s *| 8 `  H  0޽h ? 33___PPT10i.#Z+D=' = @B +9   K0 80`X(  Xr X S ت 8 `   r X S  8` `  LB  X c $D0 @@0 LB X c $D` LB X c $D` ` LB X c $D` LB X c $DH X 0޽h ? 3fff___PPT10i.2Pz+D=' = @B +   K0  .(  r  S 콶 8 `   r  S  8``    6PP L"02f